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Cirugía Cardiaca en México

ISSN 2448-5640 (Print)
Diario Oficial de la Sociedad Mexicana de Cirugía Cardiaca, A.C., y del Colegio Mexicano de Cirugía Cardiovascular y Torácica, A.C.
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2023, Number 2

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Cir Card Mex 2023; 8 (2)

Left atrial isomerism: 10-year surgical outcomes at a single center

Ortega-Zhindón DB, Calderón-Colmenero J, García-Montes JA, Pereira-López GI, Gutiérrez-Lugo A, Cervantes-Salazar JL
Full text How to cite this article

Language: English
References: 23
Page: 32-36
PDF size: 263.88 Kb.


Key words:

Congenital heart disease, Heterotaxy syndrome, Left atrial isomerism.

ABSTRACT

Introduction. Left atrial isomerism (LAI) is a complex entity with various treatments and outcomes. The aim of the study was to analyze the surgical outcomes of patients with LAI undergoing cardiac surgery. Methods. A retrospective study was carried out on patients with a diagnosis of LAI who underwent cardiac surgery were included, between January 1, 2010 and March 31, 2020. The demographic characteristics and perioperative conditions were described. Results.Twenty- seven patients were included; the median age was 6 years (IQR 3 -11), 40.7% males. The main diagnoses in patients undergoing the univentricular approach were atrioventricular canal (25.9%) and pulmonary atresia (11.1%), while cases undergoing the biventricular approach were atrial septal defect (44.4%) and ventricular septal defect (40.7%). The most common surgical procedures were modified Blalock–Taussig shunt (18.5%) in the univentricular approach and repair of septal defects (4.6%) in the biventricular approach. No early or late deaths were found. Conclusions. The survival of LAI in our center is similar to that of other referral centers. Patients with LAI must undergo a rigorous evaluation to determine an appropriate surgical strategy.


REFERENCES

  1. Calderón J, Cervantes J, Curi P, Ramírez S. Problemática de las cardiopatíascongénitas en México. Propuesta de regionalización. Arch Cardiol Mex. 2010;80(2):133-140.

  2. Cervantes J, Calderón J, Ramírez J, et al. El Registro Mexicano de Cirugía Cardíaca Pediátrica. Primer informe. Evid Med Invest Salud. 2014;7(2):56-62.

  3. Madrigal S, Bonilla C, Sánchez E. Heterotaxia: Situs ambiguo, síndrome de Ivermark o síndrome de asplenia-poliesplenia. Rev. clín. esc. med. UCR-HSJD.2019;9(2):70-76.

  4. Kim SJ. Heterotaxy syndrome. Korean Circ J. 2011;41(5):227-232.

  5. Loomba RS, Hlavacek AM, Spicer DE, Anderson RH. Isomerism or heterotaxy:which term leads to better understanding?. Cardiol Young. 2015;25(6):1037-1043.

  6. Icardo J, García J, Ros M. Malformaciones cardíacas, heterotaxia y lateralidad.Rev Esp Cardiol. 2002; 55(9):962-974.

  7. Carro A, Santamarta E, Martín M. Síndrome de heterotaxia. Cardiocore.2011;46(2):23-26.

  8. Friedberg MK, Silverman NH, Moon-Grady AJ, et al. Prenatal detection of congenital heart disease. J Pediatr. 2009;155(1):26-31.

  9. Pepes S, Zidere V, Allan LD. Prenatal diagnosis of left atrial isomerism. Heart.2009; 95(24):1974–1977.

  10. Lai WW, Geva T, Shirali GS, et al. Task Force of the Pediatric Council of the American Society of Echocardiography; Pediatric Council of the American Society ofEchocardiography. Guidelines and standards for performance of a pediatric echocardiogram: a report from the Task Force of the Pediatric Council of the AmericanSociety of Echocardiography. J Am Soc Echocardiogr. 2006;19(12):1413-1430.

  11. Carrillo-Álvarez A, Martínez-Gutiérrez A, Salvat-Germán F. Reconocimiento delniño con riesgo de parada cardiorrespiratoria. An Pediatr (Barc). 2006;65(2):147-153.

  12. Faraoni D. Definition of postoperative bleeding in children undergoing cardiacsurgery with cardiopulmonary bypass: One size doesn't fit all. J Thorac CardiovascSurg. 2018;155(5):2125-2126.

  13. Chen W, Ma L, Cui H, et al. Early and middle term surgical outcomes in patientswith heterotaxy syndrome. Cardiology. 2016;133(3):141-146.

  14. Jacobs JP, Pasquali SK, Morales DL, et al. Heterotaxy: lessons learned about patterns of practice and outcomes from the congenital heart surgery database of thesociety of thoracic surgeons. World J Pediatr Congenit Heart Surg. 2011;2(2):278-286.

  15. Baban A, Cantarutti N, Adorisio R, et al. Long-term survival and phenotypicspectrum in heterotaxy syndrome: A 25-year follow-up experience. Int J Cardiol.2018;268:100-105.

  16. Alongi AM, Kirklin JK, Deng L, et al. Surgical Management of Heterotaxy Syndrome: Current Challenges and Opportunities. World J Pediatr Congenit HeartSurg. 2020;11(2):166-176.

  17. Loomba RS, Nijhawan K, Anderson R. Impact of Era, Type of Isomerism, andVentricular Morphology on Survival in Heterotaxy: Implications for TherapeuticManagement. World J Pediatr Congenit Heart Surg. 2016;7(1):54-62.

  18. Bhaskar J, Galati JC, Brooks P, et al. Survival into adulthood of patients withatrial isomerism undergoing cardiac surgery. J Thorac Cardiovasc Surg.2015;149(6):1509-1513.

  19. Vigneswaran TV, Jones CB, Zidere V, et al. Effect of Prenatal LateralityDisturbance and Its Accompanying Anomalies on Survival. Am J Cardiol.

  20. 2018;122(4):663-671.20. Alsoufi B, McCracken C, Schlosser B, et al. Outcomes of multistage palliation ofinfants with functional single ventricle and heterotaxy syndrome. J Thorac Cardiovasc Surg. 2016;151(5):1369-1377.

  21. Gilljam T, McCrindle BW, Smallhorn JF, Williams WG, Freedom RM. Outcomesof left atrial isomerism over a 28-year period at a single institution. J Am CollCardiol. 2000;36(3):908-916.

  22. Banka P, Adar A, Schaetzle B, Sleeper L, Emani S, Geva T. Changes in prognosisof heterotaxy syndrome over time. Pediatrics. 2020;146(2):e20193345.

  23. McGovern E, Kelleher E, Potts JE, et al. Predictors of poor outcome amongchildren with heterotaxy syndrome: a retrospective review. Open Heart.2016;3(2):e000328. doi:10.1136/openhrt-2015-000328.




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Cir Card Mex. 2023;8