Quispe-Fernández LA, Luna-Valdez CM, Gutiérrez-Ospina A, Carrillo-González ML, Martínez-Olivares J, Monroy-Hernández VM

Language: Spanish
References: 7
Page: 86-88
PDF size: 264.40 Kb.

ABSTRACT

Primary synovial sarcoma of the heart is a very rare entity, little known for the limited number of cases. It occurs very frequently in young patients, predominantly in right-sided cardiac chambers with a lethal behavior. Survival is approximately 6 months without treatment. We describe herein a case of a 9-year-old patient with primary cardiac synovial sarcoma dependent on the right atrium. At the same time, we discuss here the clinical characteristics, surgical findings, therapeutic, echocardiographic, pathological and histological alternatives, with a lack of a high level of evidence due to the incidence of the problem and the few number of reported cases.

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