2022, Number 2
Anesthetic Management for a pregnant woman with Morquio syndrome
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Language: Spanish
References: 9
Page: 1-8
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ABSTRACT
Introduction: Morquio syndrome is an autosomal recessive hereditary disease that affects, to different extents, carbohydrate metabolism, which obstructs the ability to break bonds of long chains of glycosaminoglycans, causing mucopolysaccharides accumulation in different tissues of the human body.Objective: To describe the anesthetic management of a pregnant woman with Morquio syndrome.
Case presentation: This is the case of a 30-year-old primigravid pregnant woman, of black skin, 103 cm of height and 33 kg of weight. She came for preoperative consultation because she was pregnant at term and had low body size; the pregnancy was terminated through the abdominal route. A preanesthetic assessment was performed, which permitted to observe a history of genetic disease and previous admission for high blood pressure. The patient was allergic to dipyrone.
Conclusions: Among patients with mucopolysaccharidosis, there is a high incidence of difficulty for ventilation and endotracheal intubation associated with cardiopulmonary insufficiency. Spinal involvement represents additional difficulties for anesthesiologists. Any elective surgery requires preoperative assessment of anesthesiologic risk factors and the availability of a spectrum of airway management equipment. Anesthetic managment should be performed by a team experienced in airway management.
REFERENCES
Crespo Vallejo Dayssy Viviana, Rodríguez Pacheco Valeria Alexandra, Ruiz Ayerve Mayra Alejandra. Síndrome de Morquio, una afección infrecuente. Rev Eug Esp. 2021 [acceso: 31/10/2021];15(1):66-72. Disponible en: http://scielo.senescyt.gob.ec/scielo.php?script=sci_arttext&pid=S2661-67422021000100066&lng=es1.
Hung S, Hernández G, Briceño Y, Silvestre R, Barrios MC. Síndrome de Morquio como causa infrecuente de talla baja desproporcionada: Enfoque fisiopatológico, diagnóstico y terapéutico. A propósito de un caso. Rev Vene Endocrinol Metab. 2016 [acceso: 07/11/2021];14(3):217-25. Disponible en: http://ve.scielo.org/scielo.php?script=sci_arttext&pid=S1690-31102016000300007&lng=es3.
Lucio Medina IM, Rincón Sánchez O, Pizaña Vázquez SA, Peña García I, López García R. Síndrome de Morquio en cesárea bajo anestesia general: reporte de un caso. Anest. Méx. 2019 [acceso: 07/11/2021];31(1):56-61. Disponible en: http://www.scielo.org.mx/scielo.php?script=sci_arttext&pid=S2448-87712019000100056&lng=es6.