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Revista Cubana de Reumatología

ISSN 1817-5996 (Electronic)
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2022, Number 4

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Rev Cub de Reu 2022; 24 (4)

From limb weakness to a systemic involvement: Poems syndrome case two report and review of the literature

Rodríguez SE, Sarmiento PDA, Bernal BA, Cano MLA, Usma VAF, Saldarriaga RLM
Full text How to cite this article

Language: Spanish
References: 10
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Key words:

polyneuropathy, organomegaly, endocrinopathy, monoclonal gammopathy, POEMS síndrome.

ABSTRACT

POEMS syndrome is a rare and infrequent paraneoplastic syndrome, which occurs mainly in the sixth decade of life, characterized by multisystem involvement with a predominance of demyelinating neuropathy, which encompasses diverse and heterogeneous clinical manifestations and whose diagnosis requires a high index of suspicion. We present two cases of patients who consulted due to unusual symptoms and whose loss of strength led to an approach due to multisystem involvement that concluded with the diagnosis of this disease.


REFERENCES

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  2. Talbot A, Jaccard A, Arnulf B. Syndrome POEMS: diagnostic, prise en charge et traitements. Rev Med Interne (French). 2021;42(5):320-9. DOI: https://doi.org/10.1016/j.revmed.2021.02.0072.

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Rev Cub de Reu. 2022;24