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Órgano oficial de la Universidad Autónoma de Sinaloa

2025, Number 1

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Rev Med UAS 2025; 15 (1)

Dermatomyositis and erythroderma: Clinical case

Rodríguez-Gutiérrez JS, Valenzuela-Marrufo RA, Piña-Lugo F, Escalante-López LY, Cázares-Coss y León VY

Language: Spanish
References: 18
Page: 30-35
PDF size: 242.76 Kb.


ABSTRACT

Introduction: Dermatomyositis is an autoimmune inflammatory disease that primarily affects the skin and muscles. It presents in two age groups, a juvenile variant and a classic form observed in adults, with the latter being associated with a 30% risk of malignancy. There is a small group of patients who exhibit an erythrodermic form, affecting the majority of the body's surface, with very few cases reported in medical literature. This report describes a case of this uncommon form and provides a brief review of published cases to date. Clinical Case: A 73-year-old female patient presented with a disseminated dermatosis affecting all body segments bilaterally, displaying a polymorphic rash primarily characterized by erythema and fine scales, accompanied by intense itching. A skin biopsy was performed, and the findings were consistent with dermatomyositis, leading to the initiation of treatment with immunosuppressants with a favorable response. Conclusions: Consistent with the limited prior reports in the literature, there are very few cases documented of erythrodermic dermatomyositis. This report presents a case of this variant with a positive response to standard treatment.


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