Quijada UZM, Quijada UEE

Language: Spanish
References: 6
Page: 124-128
PDF size: 215.10 Kb.

ABSTRACT

Desmoid tumors (DT), also known as aggressive fibromatosis, are rare soft tissue neoplasms originating from fibroblasts. Characterized by locally invasive growth without metastasis, they can affect adjacent organs and structures, significantly impacting patients’ quality of life. These tumors are uncommon, with a low incidence and a predilection for women around 35 years of age. Diagnosis can be challenging due to their variable morphology and clinical presentation.
We report the case of a 38-year-old female patient with a chronic dermatosis on her left shoulder, presenting as a deep-seated solid neoformation associated with pain and erythematous-violaceous skin changes. Immunohistochemical analysis confirmed the diagnosis of dt, which was treated with wide surgical excision and adjuvant radiotherapy.
Due to their infiltrative nature and high risk of recurrence, these neoplasms necessitate a multidisciplinary approach. Immunohistochemistry plays a crucial role in diagnosis, and treatment should be individualized given the absence of standardized protocols.

REFERENCES

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