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ISSN 2539-0859 (Electronic)
ISSN 0120-8411 (Print)
Asociación Colombiana de Otorrinolaringología y Cirugía de Cabeza y cuello, Maxilofacial y Estética Facial (ACORL)

2025, Number 2

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Acta de Otorrinolaringología CCC 2025; 53 (2)

Extranodal N/K cell non-Hodgkin lymphoma nasal: An atypical case report

Macías-Fernández B, Guzmán-Romero AK, Macías-Valle LF

Language: Spanish
References: 10
Page: 171-175
PDF size: 372.61 Kb.


ABSTRACT

Introduction: Extranodal NK/T cell lymphoma (ENKTL) is a rare subtype of non- Hodgkin lymphoma Epstein-Barr virus associated. The pathogenesis of these lesions is not completely known. Objectives: To present an atypical case of nasal extranodal NK T-cell lymphoma. Materials and methods: We present the case of a 37-yearold patient with a diagnosis of extranodal nasal NK/T cell lymphoma with clinical symptoms and radiological images, which looks like a vascular tumor. Pre-surgical embolization was performed due to the high vascularity found on the tomography. The lesion was completely resected endoscopically, the patient received chemotherapy and radiotherapy, currently in remission with a two-year follow-up. Discussion: NK/T cell lymphomas are rare sinonasal tumors. Radiologically, they are locally invasive with extension to adjacent structures; they do not usually present as hypervascularized lesions. Conclusions: The detection of these tumors represents a challenge. Early diagnosis confers a better prognosis and response to treatment.


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