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2025, Number 3

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Dermatología Cosmética, Médica y Quirúrgica 2025; 23 (3)

Epidermolysis bullosa. A mucocutaneous disease

Lomelí VR, Lara BJC, Durán GLA, García RMT

Language: English
References: 30
Page: 216-220
PDF size: 265.74 Kb.


ABSTRACT

Epidermolysis bullosa corresponds to a term that encompasses a group of rare genodermatoses characterized by mechanical fragility of the skin and mucous membranes. It is characterized by the appearance of blisters and, subsecuently, erosions, scabs and scars on the skin and mucous membranes following minimal trauma. Stomatological manifestations are the most frequent after dermatological ones. Therefore, knowledge of its manifestations at both levels is essential to provide adequate treatment and follow- up. In this article, we report the findings described in the literature to date regarding the oral or stomatological manifestations in patients with epidermolysis bullosa, as well as the currently recommended interventions for their treatment and follow-up.


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