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2025, Number 2-3

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Alerg Asma Inmunol Pediatr 2025; 34 (2-3)

Phlegmasia cerulea dolens in a pediatric patient diagnosed with antiphospholipid syndrome. Case report

García-Torres KI, Waldo-Reyes R, Hernández-González CA, Azamar-Jacome AA

Language: Spanish
References: 24
Page: 67-72
PDF size: 1045.47 Kb.


ABSTRACT

Phlegmasia cerulea dolens (PCD) is a rare but serious disease related to primary or secondary hypercoagulability states. In adulthood it has been associated with malignancies, major surgery, prolonged immobilization or hormonal therapy. There are reports in children which associates it to trauma or infection. PCD presents with acute pain, massive swelling and progressive cyanosis due to venous congestion and fluid sequestration. Early diagnosis is critical for reducing overall morbidity and mortality. We present the case of a girl with severe deep venous thrombosis associated with antiphospholipid syndrome.


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