Andrade MR, García EA, De la Cruz TA, Arteche PM, Machado RA

Language: Spanish
References: 6
Page: 405-408
PDF size: 93.19 Kb.

ABSTRACT

Introduction: The neonatal epileptic encephalopathy includes two severe types of epileptic syndromes. We report a clinical and pathological study of three patients who had suffered from this epileptic syndrome since the neonatal stage. Conclusion: Two of them had inheritable metabolic disorders: one who had an ornithin-transcarbamilase deficit and the other one had methyl-malonic aciduria. The third patient showed a cerebral structural abnormality rendering to Otahara’s syndrome.

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