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1998, Number 2

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Rev Mex Pediatr 1998; 65 (2)

Experiencia en el manejo de niños con atresia de vías biliares

Escobedo VMM, Zárate HMC, Zárate GM, Galván CA, Ábrego MV, Rodríguez MC

Language: Spanish
References: 15
Page: 65-67
PDF size: 109.99 Kb.


ABSTRACT

We reviewed 10 expedients of patients with biliary atresia in a period of nine years (1988-1996). We studied clinical features, diagnosis studies as well as surgery technique age at the surgey time, anatomopatologic study and their progres. Eight of all studied patients were female, their onset was at mean of 16.5 day old (1-30) presenting jaundice, acolia and colored urine, 30% presented portal hypertension. In the laboratory tests they presented altered hepatic function test and colestasis; anemia 8.9 mg/dL (4.8-12.4), 30% altered PT/PTT. Ultrasound, MRN, biliar ducts gammagraphy shown biliary atresia. Data (7/10) four patients were operated in our hospital, three survived and two of these three were operated before 60 days old (they are still alive) and one after 60 days old and died of dehydratation secondary to acute gastroenteritis, three went to liver transplantation, 30% were not candidates to surgery because they were older than six months. We conclude that Kasai surgery is the initial election treatment in these patients and should be done before 60 days old for a better prognosis.


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