Gutiérrez MJ, Venta SJA, Jaimes HV, Reyes N

Language: Spanish
References: 10
Page: 250-253
PDF size: 355.51 Kb.

ABSTRACT

The case of an 11-year old girl is presented. She had a disease of six years of evolution that began with hypotrophism of third and fourth digits of the left hand and left hemithorax. One year after, she presented gluteal and right lower limb asymmetry, with lessening of the ipsilateral axillary fold and scapular region with a mild clear brown color at submammalian region. She besides had finger contracture in the right hand when she writes, with a scissors pattern and lack of desterity. She was previously studied at her born place and was sent to Pediatric Neurology Service without a precise diagnose, although physicians had oriented diagnose towards spinal or radicular pathology. With the examination, hypothrophysm zones and lessening of the annex with skin of augmented consistency and decreasing of compliance were corroborated. Myelopathy and multiple radiculoneuropathy were discarded and finally it was concluded that the signs and symptoms of the disease corresponded with «morphea» (localized sclerodermia). Here are analyzed mechanisms of changes in trophism either of central and peripheral origin, sclerodermia (morphea), clinical conduct and treatment.

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