Dedieu N, Cazzaniga M, Retamar JM, Muñoz BM, Abelleira C, Bermúdez CR, Casanova M

Language: Spanish
References: 0
Page: 145-148
PDF size: 119.11 Kb.

ABSTRACT

The Fontan operation is the preferred palliative surgery in patients with congenital heart disease that deals with functionally univentricular hearts, included such exceptional cases as the ones with only one pulmonary artery to one lung. Cyanosis is not an exceptional in this patients´s evolution. And it can be due to several factors. We present the case of a young woman with univentricular heart physiology and an only lung able to receive systemic flow, total cavopulmonary connection (in 2 steps) with intentional exclusion of hepatics veins from the pulmonary circulation whom extern conduct had be occluded with an Amplatzer device. In her evolution she develops portal vein and retroperitoneal pelvic veins dilatation. with hepatoportal fistulas and hepatomegalies and a severe stenosis of prehepatic inferior caval vein as consequence of Fontan´s external conduct occlusion with an Amplatzer device.