González-Ramos LA, López-Cervantes G, Rascón-Alcantar A, Castillo-Aldaco JD, Ruíz-Bustamante NP

Language: Spanish
References: 11
Page: 3-9
PDF size: 275.27 Kb.

ABSTRACT

Introduction. The congenital heart disease type total anomalous pulmonary venous connection is a condition that there is no pulmonary venous connection to the left atrium and four veins connect to the systemic venous circulation through one of its tributaries or directly to right atrium. It represents approximately 1% of all congenital heart disease.
Object. Report the experience in the diagnostic and medical-surgical treatment with this congenital heart disease. The hearts of autopsy studies with this anomalies were examined and we present anatomic finding.
Material and Methods. We reviewed the clinical records and chest x ray, electrocardiogram echocardiogram and cardiac catheterization. The hearts were examined by ourselves and we described the anatomic characteristic of each one.
Results. In a period of 1994 to 2004 we found fifteen cases of cardiac malformation type total pulmonary vein anomalous connection. The most frequent variety of this type of malformation was the supracardiac in 73%. Actually the surgical mortality is 38%. The hearts of autopsy studies were supracardiac and coronary sinus cardiac variety.
Discussion. This cardiac malformation is a rare malformation in our hospital. The supracardiac variety was the most common similar to others reports. The specific diagnoses of this condition, was made by Pediatric-Cardiologist on his opportune participation because the patients had signs and symptoms of congenital heart disease. The socioeconomic factors, pulmonary complications, malnutrition and time of waiting to surgery had influence in the mortality. Coexistence of noncardiac anomaly might cast a shadow over prognosis.
Conclusion. In the future we hope to have more technology and to have the opportunity to do surgery on time and to acquire medical and surgical experience to reduce the complications and mortality.

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