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Patología Revista Latinoamericana

2008, Number 1

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Patol Rev Latinoam 2008; 46 (1)

Turcot´s syndrome. Case report

Torres NMGJ, Rojas OS, Gutiérrez M, Anda GJ

Language: Spanish
References: 12
Page: 28-31
PDF size: 240.36 Kb.


ABSTRACT

Turcot’s syndrome is a rare hereditary disease characterized by primary brain tumors associated with colonic polyposis. The purpose of this work is to describe a case of a 16 years old girl with colonic adenocarcinoma, multiform glioblastoma and a second colonic adenocarcinoma originated in a tubular-vellous polyp, with four extra polyps. The treatment of Turcot’s syndrome is multidisciplinary, and several advances in its molecular biology have been achieved.


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