Quezada CG, Quezada CSE, Mercado PG, Durán BM

Language: Spanish
References: 13
Page: 274-276
PDF size: 100.70 Kb.

ABSTRACT

Hallervorden-Spatz disease is a metabolic disorder rare autosomal recessive. Characteristic of this disease are pigmentation degeneration of globus pallid, substantia nigra and red nucleus. In 1992 went described for first time in 5 students that presented clinical manifestations of bradypsychia, dysarthria, athaxic walk, spasticity, tremors, dystonic (digestive and respiratory), mental deterioration and visual alteration. Diagnostic realize in base to image study, magnetic resonance is the best. In this study we can to watch hypotenses images to basal nucleus level with central hyperintensity and “eye of tiger” denominated, that indicate iron deposit and neuro-axonal degeneration.

REFERENCES

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