Gutiérrez SE, Ortiz LJB, Argüelles CJ

Language: Spanish
References: 4
Page: 68-71
PDF size: 182.15 Kb.

ABSTRACT

Kaposiform hemangioendothelioma is an aggressive and rare tumor. Although it seems a benign tumor from a histological perspective, it has a high mortality without treatment. A complete exploration of the skin may show telangiectasis or equimosis, key to suspect Kasabach-Merritt syndrome. Images with magnetic resonance show a tumor with badly delimited edges with high tissue infiltration. The blood vessels that nurture or drain the tumor are comparatively scarce compared to common hemangiomas. Histology regards this with Kaposi sarcoma and shows a lobulillar infiltration of endothelial cells. A 13 year-old female with a highly aggressive and infiltrated lesion in the right elbow is presented. Hemangioendothelioma was reported in the study in histopathology. Resection and reconstruction were performed with convergent cutaneous distraction with Steinman wires. The patient evolved with tumor recidivating, and required upper limb amputation up to the third medium of the humerus.

REFERENCES

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