2010, Number 1
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Rev Mex Cardiol 2010; 21 (1)
Sinus venosus atrial septal defect and severe pulmonary hypertension. Case report
Paniagua MME, Villalobos SJA, Herrera MA, Castaño GR
Language: Spanish
References: 9
Page: 31-38
PDF size: 970.67 Kb.
ABSTRACT
We report a case of 61 year male, born in Mexico City. Diabetic since 2000 in treatment with glimepiride 2.0 mg daily. He had a cardiovascular history of congenital heart disease in Hospital La Raza without a specific diagnostic. Patient arrived to our hospital, and he was diagnosed with sinus venosus septal atrial defect with severe pulmonary hypertension. We know that atrial septal defect in adults has high incidence and sinus venosus septal atrial defect represents a third place with prevalence.of 5.0 %. Even do, in the majority of the cases the treatment is surgical, some of them still have chronic symptoms, because of right ventricular dilatation and severe pulmonary hypertension, present in 15-30% of adults with congenital heart disease, associated with increased mortality. That’s why the importance of risk stratification in congenital heart disease with high pulmonary hypertension, in the way to avoid complications and a worst prognosis after surgery.
REFERENCES
Moss-Adam. Heart Disease in infants, childrens and adolescents, 7th edition. Lippincott Williams and Wilkins. New York. 2007.
Jost CHA, Connolly HM, Danielson GK. Sinus venosus atrial septal defect: Long-term postoperative outcome for 115 patients. Circulation 2005; 112: 1953-1958.
Steele PM, Fuster V, Marc C. Isolated atrial septal defect with pulmonary vascular obstructive disease long-term follow-up and prediction of outcome after surgical correction. Circulation 1987; 76: 1037-1042.
Suchon E, Tracz W, Podolec P. Atrial septal defect in adults: echocardiography and cardiopulmonary exercise capacity associated with hemodynamics before and after surgical closure. Interact CardioVasc Thorac Surg 2005; 4: 488-492.
Landzberg MJ. Congenital Heart Disease Associated Pulmonary Arterial Hypertension. Clin Chest Med 2007; 28: 243-253.
Zamanian RT, Haddad F, Doyle RL. Management strategies for patients with pulmonary hypertension in the intensive care unit. Crit Care Med 2007; 35: 2037-2050.
Rubenfire M, Bayram M, Hector-Word Z. Pulmonary hypertension in the critical care setting: Classification, pathophysiology, diagnosis, and management. Crit Care Clin 2007; 23: 801-834.
Dimpna CA, Pujol M. Hipertensión pulmonar en el postoperatorio de cirugía cardiaca en cardiopatías congénitas: fisiopatología, clínica y manejo. Anales de Cirugía Cardiaca y Vascular 2004; 10(4): 230-238.
McLaughlin VV, McGoon MD. Pulmonary arterial hypertension. Circulation 2006; 114: 1417-1431.