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>Journals >Cirugía y Cirujanos >Year 2010, Issue 2


Valdivia-Gómez GG, Soto-Guerrero MT, Cedillo-de la Cruz MI
Sarcoma de Ewing extraesquelético que semeja abdomen agudo
Cir Cir 2010; 78 (2)

Language: Español
References: 31
Page: 163-166
PDF: 230.94 Kb.

[Full text - PDF]

ABSTRACT

Background: Extra-osseous Ewing’s sarcoma is a rare tumor of neuroectodermal origin. It presents mainly in the soft tissue of the extremities and thorax. Histologically, it is similar to Ewing’s sarcoma of the bone.
Clinical case: We present the case of a male who arrived at the emergency room with acute abdomen, leucocytosis and imaging techniques (abdominal ultrasound and computed tomography) suggestive of complicated diverticular disease. He was treated with emergency surgery. Intraoperative findings were an unsuspected tumor (20 × 15 × 15 cm). Treatment consisted of extirpation of the tumor, separating it from the adjacent viscera and followed by chemotherapy based on epirubicin, cyclophosphamide and vincristine for six cycles. Because the control abdominal CT demonstrated tumor activity in the retroperitoneum adjacent to the ascending colon and cecum, further resection was decided upon.
Conclusions: In a review of the literature, no previous reports of extra-osseous Ewing’s sarcoma were found presenting as acute abdomen. Due to the rarity of this tumor, only case reports or series have been found in the literature without randomized or comparative studies. Surgery was the cornerstone of treatment, without reports of preoperative chemotherapy. If the patient’s condition permits, percutaneous needle biopsy is mandatory to obtain optimum treatment as well as to improve the prognosis.


Key words: Ewing’s sarcoma, soft tissue tumor, primitive neuroectodermal tumor, neuroepithelial tumor, abdominaltumor, acute abdomen.


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