Cortés FRI, Garduńo ER, Velasco LEC

Language: Spanish
References: 0
Page: 400-403
PDF size: 699.82 Kb.

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The Papillon-Lefévre Syndrome is a rare syndrome that appears in 1 to 4 per million of born alive children. It is characterized by erythematous palmoplantar hyperkeratosis, and severe periodontal disease, that affects both dentitions and lead to the total loss of the teeth in early age. Here we described a 14 years old female patient; who was seen in the clinic of Pediatric Dentistry. The medical history revealed the parents consanguinity. In the clinical exam she presented erythematuos hyperkeratosis on palm and soils, periodontal inflammation, as well as severe dental mobility, she was diagnosed with Papillon Lefévre Syndrome. Unfortunately because the disease was too severe, it was not possible to maintain the teeth. Once the teeth were extracted, an immediate removable full denture was made, the periodontal healing was adequate. After three months a definitive full denture was made and the patient was placed in a year recalled program. The early identification of the syndrome plays an important roll, since the permanency of the teeth can be prolonged for a longer period in the oral cavity.