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2011, Number 1

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Rev Mex Pediatr 2011; 78 (1)

(Medullary sponge kidney associated to a double pyelocalyceal system)

Urdaneta CE, Pérez MC, Hernández UR, Flores ADC, Urdaneta CAV, Godoy BEY

Language: Spanish
References: 26
Page: 21-24
PDF size: 174.91 Kb.


ABSTRACT

The medullary sponge kidney is a rare entity, predominantly in women and is characterized by cystic malformation of the distal collecting tubules. It is usually asymptomatic, being the hematuria (micro or macroscopic), recurrent urinary tract infections and kidney stones, the most important clinical manifestations. Intravenous urography is the technique of choice for diagnosis, which allows to observe thickening pyramidal caliceal dilatation and presence of intraductal stones. His long-term prognosis is favorable, although in some cases the persistence and seventy of clinical manifestations, can lead to chronic kidney disease. The purpose of this paper is to present this rare kidney disease in a child with recurrent urinary tract infections, who also had a double pyelocalyceal system left and review the literature in this regard.


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