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Organo Oficial de la Sociedad Mexicana de Urología

2011, Number 1

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Rev Mex Urol 2011; 71 (1)

Angiomiolipoma renal atípico epitelioide

Orlich-Castelán C, Zamora-Montes de Oca MJ

Language: Spanish
References: 9
Page: 36-39
PDF size: 216. Kb.


ABSTRACT

A very rare case of atypical bilateral giant epithelioid renal angiomyolipoma in a twenty-six-year old woman is presented. Patient was asymptomatic. Imaging studies detected large masses in both kidneys and there was no evidence of hereditary diseases such as tuberous sclerosis or von Hippel-Landau disease. Left total nephrectomy and right partial nephrectomy were performed. Pathological report described various large non-encapsulated nodular tumors with local fat and adjacent renal parenchyma invasion. The largest tumor was in the left lower pole and measured ten by six centimeters in diameter. Histological report stated small vein invasion by malignant cells near the renal hilum with no evidence of renal carcinoma. There has been no distant metastasis at three-year follow-up.


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