Reyes MT, Aguilar S, Corona R, Vega I, Montalvo CC, García RG

Language: Spanish
References: 15
Page: 79-87
PDF size: 613.71 Kb.

ABSTRACT

Creutzfeldt-Jakob disease is a neurodegenerative and neuroselective entity, unusually reported in Mexico. We report a case of a 66 year-old women patient with rapidly progressive dementia, associated with cerebellum syndrome, myoclonus, abnormal movements and motor dysfunction, with diagnostic studies positively suggesting Creutzfeldt-Jakob disease. The clinical characteristics and diagnostic studies are presented. A review of the literature discussing pathogenic mechanisms, variants of the disease and diagnostic clues, are also presented.

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