Sancha MLM, Alemán VP, Cruz JM, Floriano MM, Serrano ME, Aguilar LAO, Vizzuett MR

Language: Spanish
References: 10
Page: 271-277
PDF size: 152.68 Kb.

ABSTRACT

Vascular malformations incidence is very low in the general population. Hepatic vascular malformations are very rare in newborns. Such malformations are usually found as part of another condition or diagnostic approach. Size, location and time of diagnosis challenge clinicians for treatment and survival of these kinds of patients. We present the case of a female newborn from an adolescent mother, gravida I, pregnancy complicated by polihidramnios, 35 weeks of gestation, born by cesarean section due to polihidramnios and labor, with bradycardia, poor respiratory effort and cyanosis, required one cycle of IPPV, successful, admitted at Neonatal Intensive Care Unit, received intravenous solutions, glucose, electrolytes, supplementary oxygen, CPAP was changed to mandatory ventilation due to respiratory failure, started amines and plasma transfusion, surgical exploration was suspended twice, due to anemia, thrombocytopenia and prolonged clotting times, with diagnosis of Kasabach-Merritt syndrome, after convulsive episode the patient dies. Partial postmortem examination confirmed big liver and poor development of gut, histological studies confirmed hemangioendotelioma or infantile hepatic hemangioma. Due to such diagnosis, we searched the literature on the subject.

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