Bautista GEJ, Morales GV, Galván EH, Flores RAL, Vásquez SE, Pizarro ON

Language: Spanish
References: 5
Page: 663-667
PDF size: 169.74 Kb.

ABSTRACT

The Mayer-Rokitansky-Kuster-Hauser is a rare congenital anomaly characterized by lack of vaginal and uterine development variable and normal ovaries. It results from agenesis or hypoplasia Müller duct system. Cervicovaginal agenesis as part of the complex syndrome, is even rarer. We report two cases: adolescent patient with primary amenorrhea, cervicovaginal agenesis and chronic pelvic pain, and 28 patients with primary amenorrhea, congenital absence of uterus and vagina.

REFERENCES

1. Acién P, Quereda F, Santoyo T. Cervicovaginal agenesis: spontaneus gestation at term after previous reimplantation of the uterine corpus in a neovagina: Case Report. Human Reproduction 2008;23:548-553.

2. Bianchi N, Berlanda A, Bulfoni F, Fontana E. Laparoscopic creation of a neovagina and recovery of menstrual function in a patient with Rokitansky syndrome: Case report. Reproduction 2006;21:3287-3289.

3. Edmonds K. Vaginal and uterine anomalies in the pediatric and adolescent patient. Current Opinion in Obstetrics and Gynecology 2001;13:463-467.

4. Folch M, Pigem I, Konje J. Müllerian Agenesis: Etiology, Diagnosis and Management. Obstetrical and Gynecological Survey 2000;55: 644-649.

5. Giannesi A, Marchile P, Benchaib M, et al. Sexuality after laparoscopic Davydov in patient affected by congenital complete agenesis associated with uterine agenesis or hipoplasia. Human Reproduction 2005;20:2954-2957.