Enríquez VME, Cossío ZA, Velasco OEC, Cruz CE, Pacheco PE, Rivadeneira IM

Language: Spanish
References: 9
Page: 7-13
PDF size: 387.16 Kb.

ABSTRACT

Introduction: The multianeurismática disease is little well-known a pathological organization, which presents di verse aetiologies, reason why their location, morphology and forms of presentation uary from a case to another one.
Objective: To analyze and to report the casuistry ofthe Servicio de Angiología y Cirugía Vascular del HECMN "La Raza" in the diagnosis and treatment of multianeurysmatic disease.
Material and methods: A retrospectiue and descriptiue study was perfo rmed in patients with diagnosis of multianeurysmatic disease who were admitted for treatment in the Angiology and Vascular Surgery Service at the Hospital de Especialidades, Centro Médico La Raza, IMSS. The study took place during a period of three years (2001-2004). The objective of the present study was to analyze and report the incidence, clinical presentation, anatomical distribution, treatment and complications.
Results: The preset study included four patients, three male and one female, whose ages ranged from 1 to 46 years. All patients had severe high blood pressure at the moment of diagnosis. Two patients had intense headache and presented with a transient ischemic attack, the other two patients presented acute arterial insufficiency secondary to peripheral aneurism thrombosis. The four patients underwent surgery. The different histological reports were no conclusive to a specific arterial pathology.
Conclusion: Multianeurysmatic disease is a rare condition and when present, the most common etiology includes Ehlers Danlos syndrome, Marfan syndrome, Takayasu or Kawasaki arterial disease and poliarteritis nodosa among others.
Nevertheless it was not possible to establish a specific diagnosis in our series due to a lack of a reasonable coincidence between the clinical presentation and the histopathological results, therefore we considered them as idiopatic.

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