2012, Number 3
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ABSTRACTSuperficial siderosis of the central nervous system is a very infrequent disease characterized by deafness, cerebellar symptoms and pyramidal signs. This disorder is the consequence of chronic subarachnoid hemorrhage. Brain magnetic resonance imaging shows a characteristic marginal low T2-weighted signal of hemosiderin around the surface of the central nervous system. The most promising way of treating the disorder is to identify the source of bleeding and remove it; however, once the central nervous system surface is greatly affected by hemosiderin, even removing the source of bleeding will have little effect in the progression of clinical deterioration. Avoiding diagnostic delay is very important in those cases susceptible of causal treatment. We report the case of a patient with slowly progressive development of cerebellar ataxia and hearing loss due to superficial siderosis of the central nervous system.
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