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2014, Number 01

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MediSan 2014; 18 (01)

Nesidioblastosis: persistent hyperinsulinemic hypoglycemia in the childhood

Granela CK, Gutierrez MA, Medina AFE, Montesinos ET, Perón RD
Full text How to cite this article

Language: Spanish
References: 10
Page: 127-133
PDF size: 260.73 Kb.


Key words:

nesidioblastosis, persistent hyperinsulinemic hypoglycemia, subtotal pancreatectomy, pediatric hospitals.

ABSTRACT

Two case reports of female newborns are presented who, among other symptoms, presented with low concentrations of maintained glucemia (lower than 2,2 mmol/L), so they were evaluated in the Endocrinology Service of "Eduardo Agramonte Piña" Teaching Pediatric Provincial Hospital in Camagüey, where they were diagnosed nesidioblastosis-- persistent neonatal hypoglycemia --. In one of the patients the medical treatment was favorable, but in the other it was necessary to carry out a subtotal pancreatectomy. At present both patients receive therapeutic schedules adjusted to their clinical needs.


REFERENCES

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  2. Raffel A, Krausch MM, Anlauf M, Wieben D, Braunstein S, Klöppel G, et al. Diffuse nesidioblastosis as a cause of hyperinsulinemic hypoglycemia in adults: a diagnostic and therapeutic challenge. Surgery. 2007; 141(2): 179–84.

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