Pérez LH, Cisneros GLC, Barba RE

Language: Spanish
References: 6
Page: 113-117
PDF size: 159.89 Kb.

ABSTRACT

Introduction: Hemangiolymphangiomas are congenital malformations of the lymphatic and vascular system. The clinical symptom is a tumor that causes esthetic and functional troubles. The management of the patients can include monitor symptoms, sclerosing therapy and the extirpation or reduction of the volume of the tumor. The objective of this article is to state the strategic plan of giant toracoabdominal hemangiolymphangioma management in children. Clinical case: Two year old, male with giant toracoabdominal hemangiolymphangioma, prenatal detection confirmed at birth. With the preoperative projection of 100% of total body weight of patient. To admission the patient weight 27 kg, a tumor since the axilary fossa to the inguinal area and showed a collateral tumor over the left shoulder and the side face of thorax. A multidisciplinary team decided a two steps resection. The first surgery consisted of placement of venous access, invasive monitoring. a long incision and the nutrient vessels were ligated, the tumor was removed in a block, after that it was placed a drainer and the flaps were rotated. Findings tumor 15 kg, the evolution of the patient was satisfactory. Two months after, shows an increase of the left axilar lesion, so we decided to performing the surgery under the same lines that the previous. Findings: tumor of 785 g. Six months after the patient hasn’t showed signs of relapse. Discussion: Toracoabdominal hemangiolymphangioma in Childs is rare, the giant lesions and systemic troubles, requires an accurate surgical management. The case presented before was the result of a carefully planned and multidisciplinary strategy.

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