Lazo CÓA, Vanzzini GMA, Maldonado VR, Manzo PG

Language: Spanish
References: 10
Page: 84-88
PDF size: 342.27 Kb.

ABSTRACT

Introduction: Disorders of sexual differentiation formerly called hermaphroditism, has been documented since ancient times; this term refers to the presence of ambiguous genitalia ie without clear evidence of the assignable sex. The most common cause of female pseudohermaphroditism is congenital adrenal hyperplasia, an inherited disorder of adrenal steroidogenesis. Objective: The aim of this paper is to present a patient under three years of age with this diagnosis, who after being comprehensively evaluated by a multidisciplinary team of Regional Specialty Hospital del Bajio, surgical treatment was performed genitoplasty feminizing type (clitoroplasty and vaginoplasty) to give favorable results. Material and methods: Review of medical records and updated literature search. Results: Two months after surgery, patient has good general condition, with female external genitalia, normal anatomic appearance. Conclusions: All patients with disorders of sexual differentiation, must undergo a comprehensive evaluation by a committee of professionals in this area, clitoroplasty must be made early and if possible also vaginoplasty should be completed in one surgical time that during the procedure respects the neurovascular bundle, thereby retaining the sensitivity and vascularity of the clitoral glans.

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