Zarain RA, Hernández GA, Rubio BG, López DR

Language: Spanish
References: 8
Page: 178-182
PDF size: 286.54 Kb.

ABSTRACT

Background: Multiple endocrine neoplasia type 2A (MEN 2A) is a autosomal dominant inherited syndrome characterized by medullary thyroid carcinoma (MTC), pheochromocytoma and primary parathyroid hyperplasia. Pheochromocytoma is present in 40-50% of the cases. MEN 2A has an estimated prevalence of 1 in 30,000. Material and methods: We present the case of a 32-year-old female patient with history of MTC operated in 2008. Five years later, she starts with elevated blood pressure with a computed tomography showing increased volume in both adrenal glands. The biochemical profile showed an elevation in urine metanephrines (8,107 µg) and urine adrenaline (272 µg). A anterior bilateral laparoscopic adrenalectomy was performed previous α and β blockade, with an excellent outcome. Pathology report confirmed a bilateral pheochromocytoma. Conclusions: Anterior bilateral laparoscopic adrenalectomy is an effective and safe procedure for bilateral pheochromocytoma. It is associated with less postoperative pain and in-hospital stay.

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