Galve J, Fuertes I, Rebollo M, Ferrando J

Language: Spanish
References: 7
Page: 42-45
PDF size: 306.12 Kb.

ABSTRACT

Physiological cutis marmorata (PCM) is a congenital vascular anomaly that presents at birth or shortly thereafter. It is characterized by a reticular and prominent aspect of the cutaneous vascular tree. PCM resolves spontaneously with time but in those cases it is important to rouled out the cutis marmorata telangiectasica congenita (CMTC) that in the 50% of cases have been associated to other different anomalies. We report a six-years-old girl that at the age of 45 days was widely explored because the presence of cutis marmorata and hemifacial vascular malformation who subsequently developed disseminated cutaneous vascular malformations while CMTC lesions disappeared spontaneously. Recently, due to seizures, it has been shown the presence of pial angiomatosis, which restates the initial diagnosis, concluding that it is an association between Sturge-Weber syndrome, CMTC and disseminated cutaneous vascular malformation.

REFERENCES

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