Garza-Alatorre AG, Anaya-Medina G, Hernández RCD, Careaga CG, Rodríguez CJA, Acevedo TML, Rodríguez MV

Language: Spanish
References: 5
Page: 122-125
PDF size: 391.30 Kb.

ABSTRACT

Introduction: The double outlet right ventricle (DORV) is a rare malformation that represents 1-5% of all congenital heart diseases. The Taussig-Bing syndrome is the second most frequent cause of DORV, just after the Fallot type, and it is characterized by transposition of the aorta to the right ventricle and malposition of the pulmonary artery with subpulmonary ventricular septal defect (VSD). Material and methods: One-month old patient, with heart failure. Diagnosed by echocardiography as Taussig-Bing heart. Surgically intervened with total correction intraventricular tunnel with closure of the VSD + Damus-Kaye-Stansel + closure of the aortic valve + Rastelli + aortic plasty. One month later, the patient was discharged from PICU, with anticongestive treatment and follow-up visit in pediatric, pediatric cardiology and nutrition services. Discussion and conclusions: There are 3 different correctives approaches for the Taussig-Bing heart: arterial switch, Damus-Rastelli surgery or Kawashima intraventricular tunnel. There are few published cases of total correction of Taussig-Bing heart, because is a rare heart disease, with a high mortality rate, classified as score 6 in the RASCH-1 (50% mortality). The correction of complex heart disease still represents a huge challenge for the health personnel, but performing heart surgery and postsurgical care with quality, each time we will get more experience decreasing the mortality and morbidity and we will give a better quality of life to all those children who are in a waiting list to cardiac surgery.

REFERENCES

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