Ochoa-Nava R, Ballesteros-Ramos P, Espinoza-Soto G

Language: Spanish
References: 12
Page: 25-29
PDF size: 246.55 Kb.

ABSTRACT

Light-chain amyloidosis in pediatric patients is exceptional. Pediatric cases in Mexico have not been reported, so far. We present the case of a 9-month-old male infant who debuted with periorbital and lower extremities purpura, heart failure and anasarca. Clinical history, physical findings, laboratory data and diagnostic methods focused on the cardiac and histopathological approach are discussed. A review of the literature regarding the frequency of amyloidosis in the pediatric population as well as the diagnostic approach of this entity is presented. The prognosis of amyloidosis depends on the type of amyloid material, and extent and damage of the involved organs, so diagnosis and typification is crucial for the patient.

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