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2017, Number 2

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Revista Cubana de Angiología y Cirugía Vascular 2017; 18 (2)

Congenital arteriovenous fistulae in Ecuador

Hernández CCM, Gaybor LJC, Guerra VE

Language: Spanish
References: 31
Page: 167-177
PDF size: 111.45 Kb.


ABSTRACT

Introduction: Klippel Trenaunay syndrome is an infrequent congenital neurocutaneos syndrome causing vascular conditions, and characterized by angioma or nevus flammeus, asymmetric hypertrophy of soft tissue and varicose veins, although other associated alterations might be observed.
Objective: To identify the frequency and characteristics of arteriovenous fistulae in Ecuador.
Methods: Out of 3 000 patients, who were seen because of various vascular causes, 23 patients were detected and studied. They had been diagnosed with congenital arteriovenous fistulas based on clinical examination and complementary studies (of limb scanning, comparative venous blood gasometry to determine oxygen pressure and dynamic axial angiotomography. The following variables were analyzed: age, sex, location of fistulas and treatment.
Results: High frequency of fistulas (34.7 %) was found in children aged less than one year, followed by 6- 10 years age group (26 %). The most frequent location (86.6 %) was in lower limbs and medical treatment was the most widely used.
Conclusions: In Ecuador, there is high frequency of congenital arteriovenous fistulae, above all at early ages of life. Clinic study and comparative venous blood gasometry are important for the diagnosis of this disease.


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