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2017, Number 3

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Rev Mex Pediatr 2017; 84 (3)

Pulmonary capillary hemangiomatosis: a rare case of pulmonary arterial hypertension

Forero-Manzano M, Otoya-Castrillón J, Serrato-Roa F, Ojeda P

Language: Spanish
References: 12
Page: 116-119
PDF size: 340.94 Kb.


ABSTRACT

Pulmonary capillary hemangiomatosis (PCH) is a rare cause of primary pulmonary hypertension. About 100 cases have been reported, of which a few are newborns, in whom diagnosis can be a challenge. We present the case of a two-month-old female patient with pulmonary capillary hemangiomatosis who presented cardiac arrest as the first manifestation. We also review the medical literature regarding new discoveries that could explain its development. To our knowledge, this is one of the few cases reported in Latin America.


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