2017, Number 4
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Rev Mex Pediatr 2017; 84 (4)
Sirenomelia sequence. Clinical and radiological findings of three cases
Pérez-García G, Ornelas-Arana ML, López-Pérez LG, Ávalos-Huízar XA, González-Pérez G
Language: Spanish
References: 7
Page: 154-157
PDF size: 207.45 Kb.
ABSTRACT
Introduction: Sirenomelia sequence is a congenital
disorder characterized by the fusion of the lower limbs;
its prevalence in the Mexican population is about 2.36 in
100,000 births.
Patients and methods: We report three
cases with sirenomelia sequence and we describe the clinical
and radiological findings of each one.
Results: The cases described correspond to the types III, IV and VI of the Stocker and Heifetz classification; it is worth highlighting short and
asymmetric thorax, platybasia, ovoid and sinostotic vertebrae
and ribs, duplicated and extra ribs, which are findings
previously non-reported.
Conclusions: A timely diagnosis of
sirenomelia sequence allows the optimized attention of the
patient and counseling of the parents, considering the bad
prognosis of this disease.
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Chavez-Corral DR, Aguilar-Torres CR, Levario-Carrillo M, Alcalá- Sanchez I, Fierro-Murga R, Arámbula-Almanza J et al. Sirenomelia apus: reporte de un caso clínico. Ginecol Obstet Mex. 2011; 79: 501-507.
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