Zatarain-Gulmar A, Ramírez-Vilchis AN

Language: Spanish
References: 14
Page: 288-292
PDF size: 264.96 Kb.

ABSTRACT

Holopronsencephaly is a complex brain malformation resulting from the incomplete división of the prosencephalon, which in turn generates total or partial nonseparation of the brain hemispheres. Even though it is considered the most common brain and face malformation in humans conceptions wise (1 in every 250), the incidence drastically diminishes to less than 1 in every 10,000 live births. The objective of this article is to present the case of a 1 year and 9 months old patient that suffers the semilobar variant of this pathology, its imaging characteristics, associated findings, risk factors, different classifications, as well as a brief discussion of the recent literature available about the semilobar variant of this entity.

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