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2019, Number 5

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Rev Clin Esc Med 2019; 9 (5)

Adult-Onset Still’s Disease

Camacho SAE, Montero SG, Vega CJC
Full text How to cite this article

Language: Spanish
References: 9
Page: 39-44
PDF size: 283.19 Kb.


Key words:

Adult-Onset Still’s Disease, Still’s disease, fever, rash, macrophage activation syndrome, Yamaguchi diagnostic criteria.

ABSTRACT

The adult-onset Still’s disease is an autoinflammatory polygenic rare systemic condition, nonetheless, clinically well described. Because of its sporadic presentation in adults with a potential severe inflammatory start, linked to a broad spectrum of manifestations and complications, it presents as a non-solved challenge to clinicians, with limited therapeutic options. In this article a patient´s case of the San Juan de Dios Hospital will be reviewed. Afterwards, general aspects such as clinical presentation, diagnostic criteria, associated complications y and therapeutic options will be described.


REFERENCES

  1. Giacomelli R, Ruscitti P, Shoenfeld Y. A comprehensive review on adult onset Still’s disease. Journal of Autoimmunity. 2018;93:24-36.

  2. Narula N, Narula T, Abril A. Seizing the clinical presentation in adult onset Still’s disease. An extensive literature review. Autoimmunity Reviews. 2015; 472–477.

  3. Narváez J. Adult onset Still’s disease. Med Clin(- Barc). 2018;150(9):348-353.

  4. Castañeda S, Blanco R, González-Gay M. Adult-onset Still’s disease: Advances in the treatment. Best Practice & Research Clinical Rheumatology. 2016;30(2):222-238.

  5. Mitrovic S, Fautrel B. New Markers for Adult-Onset Still’s Disease. Joint Bone Spine. 2018;85(3):285-293.

  6. Lebrun D, Mestrallet S, Dehoux M, Golmard J, Granger B, Georgin-Lavialle S et al. Validation of the Fautrel classification criteria for adult-onset Still’s disease. Seminars in Arthritis and Rheumatism. 2018;47(4):578-585.

  7. Govoni M, Bortoluzzi A, Rossi D, Modena V. How I treat patients with adult onset Still’s disease in clinical practice. Autoimmunity Reviews. 2017;16(10):1016- 1023.

  8. Sun N, Brezinski E, Berliner J, Haemel A, Connolly M, Gensler L et al. Updates in adult-onset Still disease: Atypical cutaneous manifestations and associations with delayed malignancy. Journal of the American Academy of Dermatology. 2015;73(2):294-303.

  9. Mahroum N, Mahagna H, Amital H. Diagnosis and classification of adult Still’s disease. Journal of Autoimmunity. 2014;48-49:34-37.




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Rev Clin Esc Med. 2019;9