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Federación Mexicana de Ginecología y Obstetricia, A.C.

2020, Number 01

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Ginecol Obstet Mex 2020; 88 (01)

Mayer-Rokitansky-Küster-Hauser syndrome with pelvic organ prolapse: Case report

Ramírez-Isarraraz C, Rodríguez-Colorado ES, Gorbea-Chávez V, Granados-Martínez V, Olvera-Delgado JJ, Bravo-Canales GR

Language: Spanish
References: 15
Page: 54-58
PDF size: 211.49 Kb.


ABSTRACT

Background: The Mayer-Rokitansky-Küster-Hauser syndrome, has an incidence of 1 per 4,500 to 5,000 women, is caused by an embryonic underdevelopment of the müllerian ducts, resulting in agenesis of the vagina or uterus. There is treatment based on dilatations and creation of neovagina by surgery. Prolapse of the vaginal vault in Mayer-Rokitansky-Küster-Hauser syndrome is rare and may occur after conservative or surgical treatments. The lack of vaginal support structures can lead these patients to develop a vaginal vault prolapse
Case: A 26-year-old woman, who started sexual life at 16 years of age. He came to the clinic due to a sensation of a foreign body in the genitals and vaginal bulge of two years of evolution. Physical examination: normal external genitalia without alterations, with presence of total vaginal prolapse. Reflex of the sacral plexus S2-S4 (clitoral, perineal and anal) present and normal. Pelvic organ prolapse quantification (POP Q): 0, 0, +2, 3, 4, 5, -1, -1, x. IP: II, Gossling 2. Laparoscopic sacrocolpopexy was performed and type I mesh with monofilament was used to correct vaginal prolapse. At 3 months after the procedure, she denies vaginal bulge symptom in vagina, satisfactory active sexual, denies dyspareunia.
Conclusions: Laparoscopic sacrocolpopexy with mesh placement is a treatment option with good results in the restoration of the anatomy, sexual function and satisfaction of the patient in a patient with dome prolapse posterior to the neovagina.


REFERENCES

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