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2021, Number 1

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Dermatología Cosmética, Médica y Quirúrgica 2021; 19 (1)

Granulomatosis with Polyangiitis: A Case Report

Ramírez ME, Blas HÓA, Carreño-Gayosso EA
Full text How to cite this article

Language: Spanish
References: 10
Page: 43-46
PDF size: 188.21 Kb.


Key words:

vasculitis, granulomatosis, c-anca, palpable purpura.

ABSTRACT

Systemic vasculitis are a heterogenous group of diseases affecting different organs and systems secondary to inflammation and injury of vassels.
We report a 44-year-old male patient, with diagnosis of granulomatosis with polyangiitis with mucocutaneous manifestations, presenting oral ulcers and palpable purpura on the lower extremities. He was admitted to Internal Medicine Service for diagnostic and therapeutic approach, with articular symptoms ash his initial clinical manifestation. During his hospitalization, cytoplasmic pattern (c-anca) neutrophil antibodies were positive and cutaneous biopsy was made reporting leukocytoclastic and neutrophilic vasculitis. The patient received treatment with systemic steroids and monoclonal antibody due to the severity of the condition.


REFERENCES

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  2. Pulido-Pérez A, Avilés-Izquierdo JA y Suárez-Fernández R, Cutaneous vasculitis, Actas Dermosifiliogr 2012; 103:179-91.

  3. Wetter DA, Dutz JP, Shinkai K y Fox LP, Cutaneous vasculitis. En Bolognia JL, Jorizzo JL y Schaffer JV, Dermatology, 4a ed., Pekín, Elsevier, 2018, pp. 409-39.

  4. Sunderkötter C, Lamprecht P, Mahr A, Metze D y Zelger B, Nomenclature of cutaneous vasculitides: German translation of the dermatologic addendum to the 2012 Revides International Chapel Hill Consensus Conference Nomenclature of Vasculitides, J Dtsch Dermatol Ges 2018; 16:1425-32.

  5. Ponte C, Agueda AF y Luqmani RA, Clinical features and structured clinical evaluation of vasculitis, Best Pract Res Clin 2018; 32:31-51.

  6. Lynch JP, Derhovanessian A, Tazelaar H y Belperio JA, Granulomatosis with polyangiitis (Wegener’s granulomatosis): evolving concepts in treatment, Semin Respir Crit Care Med 2018; 39:434-58.

  7. Grygiel-Górniak B, Limphaibool N, Perkowska K y Puszczewicz M, Clinical manifestations of granulomatosis with polyangiitis: key considerations and major features, Postgrad Med 2018; 130:581-96.

  8. Falk RJ, Pathogenesis of granulomatosis with polyangiitis and related vasculitides. Disponible en: https://www.uptodate.com/contents/ pathogenesis-of-granulomatosis-with-polyangiitis-and-relatedvasculitides? search=granulomatosis%20con%20poliangitis &source=search_result&selectedTitle=6~150&usage_type= default&display_rank=6. Consultado: 31 de julio de 2019.

  9. Greco A, Marinelli C, Fusconi M, Macri GF, Gallo A, De Virgilio A et al., Clinic manifestations in granulomatosis with polyangiitis, Int J Immunopathol Pharmacol 2016; 29:151-9.

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Dermatología Cosmética, Médica y Quirúrgica. 2021;19