Campos-Fernández MM, Serra E, Alomar A, Dalmau J

Idioma: Español
Referencias bibliográficas: 32
Paginas: 261-267
Archivo PDF: 474.02 Kb.

RESUMEN

La enfermedad de Darier-White es una dermatosis reportada por primera vez en 1889. Es transmitida en forma autosómica dominante y se caracteriza principalmente por pápulas hiperqueratósicas localizadas principalmente en regiones seborreicas y anormalidades ungueales. Inicia generalmente entre la primera y segunda décadas de la vida. Su diagnóstico es clínico e histopatológico y el tratamiento más efectivo es a base de retinoides orales del tipo de la isotretinoina. La mayor morbilidad causada por esta enfermedad son las consecuencias psicosociales que causa la apariencia de las lesiones y su condición crónica. Su prevalencia es variable alrededor del mundo, siendo mayor en algunos países europeos que en los países latinoamericanos. En México es una entidad tan poco frecuente que a veces es subdiagnosticada; de ahí nuestro interés por realizar esta revisión con el fin de conocer las características principales de este padecimiento para poder llevar a cabo el diagnóstico temprano y así evitar posibles complicaciones y repercusiones en todas las esferas de los pacientes con enfermedad de Darier.

REFERENCIAS (EN ESTE ARTÍCULO)

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