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2006, Número 4

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Dermatología Cosmética, Médica y Quirúrgica 2006; 4 (4)


Enfermedad de Paget extramamaria. Reporte de un caso

Gutiérrez-Vidrio RM, Cortés-Lozano N, Navarrete-Franco G, Maldonado-Cano TE, Ríos-Berumen LP

Idioma: Español
Referencias bibliográficas: 42
Paginas: 295-300
Archivo PDF: 717.77 Kb.


RESUMEN

La enfermedad de Paget extramamaria (EPEM) es una dermatosis maligna observada, sobre todo, en áreas donde existe alta densidad de glándulas apocrinas. Es una enfermedad poco frecuente, más común en el sexo femenino y en la raza blanca, con mayor incidencia en la séptima década de la vida. En este artículo se presenta una revisión de las teorías patogénicas de esta enfermedad, su cuadro clínico, histopatología, diagnóstico diferencial y tratamiento, y se presenta el caso clínico de una paciente de 78 años de edad, atendida en el Centro Dermatológico Pascua con diagnóstico de enfermedad de Paget a nivel vulvar, manejada con vulvectomía total con evolución satisfactoria.


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