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2006, Number 4

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Dermatología Cosmética, Médica y Quirúrgica 2006; 4 (4)

Extramammary Paget´s disease. A case report

Gutiérrez-Vidrio RM, Cortés-Lozano N, Navarrete-Franco G, Maldonado-Cano TE, Ríos-Berumen LP

Language: Spanish
References: 42
Page: 295-300
PDF size: 717.77 Kb.


ABSTRACT

Extramammary Paget􀀀s disease is a malignant dermatosis observed mainly in areas of high density of apocrine glands. It is a rare disease, more common in white women, with a peak of incidence in the 7th decade. We present a review of its pathogenic theories, clinical manifestations, pathology, differential diagnosis, and treatment including the case of al 78-year-old woman with vulvar Paget􀀀s disease, treated with total vulvectomy and a satisfactory evolution.


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