2022, Number 1
Univentricular heart associated with congenital atrioventricular block in an adult patient
Borges LJS, Cuevas CA, Rosas ME, Ochoa PV, Castaño GRJ, Ayala HE
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Language: Spanish
References: 7
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ABSTRACT
Univentricular heart is a rare complex cyanotic congenital heart disease, characterized by the presence of a single ventricular cavity into which both atria drain, which can present in three different morphological forms. It is caused by the absence in the formation of the interventricular septum, which causes a three chambered heart. It has a prevalence of 5 out of every 100,000 live births, predominantly in males, and it constitutes 2% of all congenital heart disease. Depending on the accompanying alterations, it is clinically manifested by cyanosis, pulmonary hypertension and congestive heart failure. It is usually associated with changes in the position of the great arteries, dextrocardia, valvular or subvalvar pulmonary stenosis, subaortic stenosis, total or partial anomalous pulmonary venous drainage, coarctation of the aorta, and congenital atrioventricular block. Diagnosis can be made from the prenatal period through fetal ultrasound, which can improve survival by performing early management, mainly surgical. We present the case of a woman with a diagnosis of univentricular heart, with permanent pacemaker due to complete congenital atrioventricular block with the aim of carrying out a detailed review of this congenital heart disease, diagnostic approach and treatment.REFERENCES