Gil-Hurtado E, García-Luna J, Balan-Can LA, Zapata-Ramayo SI

Language: Spanish
References: 13
Page: 29-33
PDF size: 705.10 Kb.

ABSTRACT

Introduction: polycystic liver disease is a rare hereditary condition which makes up 3% of benign liver lesions that results in liver cysts due to mutations in fluid transport proteins and hepatic epithelial cell growth. Rarely, it occurs in isolation without polycystic kidney disease, which has a prevalence of 0.05 to 0.13%. Clinical case: a 31-year-old female with no relevant medical history presented with a 5-month history of colicky abdominal pain in the right hypochondrium, nausea, asthenia, and adynamia. Ultrasound and computed tomography revealed multiple anechoic cysts throughout the liver parenchyma, occupying 50% of the right lobe (2,200 cm³), classified as Gigot III/Schnelldorfer type C. Renal cysts were ruled out. Laparoscopy was performed with cyst unroofing using diathermy (high-frequency currents) and aspiration of 2,300 cm³ of citrine content, without postoperative complications. The patient was discharged two days later and, at one-month follow-up, showed complete resolution of symptoms. Conclusions: polycystic liver disease is a progressive genetic condition requiring treatment in a small number of cases. Supportive management is recommended for mild symptoms, and surgical treatment for moderate or severe cases. Here we successfully treated the patient using laparoscopy and cyst unroofing.

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