Rangel-Delgado E, Vázquez-González RM, Chávez-Delgado JR, Romero-Martin SA, Martínez-Tenorio M, Luna-Espinoza LA

Language: English
References: 6
Page: 100-162
PDF size: 1212.62 Kb.

ABSTRACT

Cardiac rhabdomyosarcoma is an exceedingly rare and aggressive malignant tumor. We present the case of a 31-year-old man with dyspnea and fever, whose echocardiographic evaluation revealed a left atrial mass causing severe mitral regurgitation. He underwent partial resection, with histopathological findings of pleomorphic rhabdomyosarcoma and positive surgical margins. He received adjuvant chemotherapy with a favorable response, which led to a significant reduction in tumor size and improved cardiac function. However, survival in these neoplasms remains limited due to their high aggressiveness and delayed diagnosis.

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