Aviña FJA, Hernández ADA

Language: Spanish
References: 14
Page: 109-112
PDF size: 138.98 Kb.

ABSTRACT

Ohtahara syndrome is included in the group of epileptic encephalopathies of infancy and is characterized by convulsive disease with early appearance of epileptic seizures specially tonic and myoclonic type, having an special electroencephalographic pattern of “Burst-Suppression”. We describe a clinical case in a female infant with congenital cardiopathy and neurological affection of periventricular leukomalacia, with no response to treatment, that progressed to status epileptic and who finally died at 4 months of age.

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