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>Journals >Cirugía y Cirujanos >Year 2007, Issue 4

Rodríguez-Ortega MF, Jacobo-Valdivieso EJ, Flores-Calderón O, García-Ortegón MS, León-Hernández G, Luna-Saucedo MD
Papillary cardiac fibroelastoma. An unusual presentation
Cir Cir 2007; 75 (4)

Language: Español
References: 21
Page: 293-296
PDF: 139.33 Kb.

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Background: Papillary fibroelastoma is a rare benign tumor characterized morphologically since first being described in 1976. Nevertheless, this tumor can be presented with a variety of clinical manifestations, making diagnosis challenging for the physician. There are no gender or age preferences but it is diagnosed by site of presentation along with macro- and microscopic characteristics.
Case report: We report the case of a male patient with a history of type 2 diabetes mellitus and arterial hypertension who was admitted to the hospital with a diagnosis of ischemic heart disease accompanied by sustained ventricular tachycardia. Echocardiogram reported degree I diastolic dysfunction, apical ventricular aneurysm, and unusual apical tumor of the septum and left ventricle.
Discussion: Primary heart tumors have an incidence of 0.0017 %. The most common symptoms are chest pain, syncope, dyspnea and arrhythmias. Diagnosis is accomplished incidentally by echocardiography, which is usually carried out for other reasons. Surgical procedure of choice is total tumor resection along with valve repair or replacement, if necessary, and in some cases cardiac endothelium resection and repair, with or without pericardium patch replacement.
Conclusions: Papillary fibroelastoma is rare but is a recognized cause of embolic phenomena. Rapid identification followed by surgical resection is curative, precise and well tolerated by the patient.

Key words: Papillary cardiac fibroelastoma, benign cardiac tumor, left ventricle.


  1. 1. Alfaro-Gómez F, Argüero-Sánchez R, Careaga-Reyna G. Tumores cardiacos. Experiencia de 16 años en el Hospital de Cardiología del Centro Médico Nacional Siglo XXI. Cir Ciruj 2003;71:179-185.

  2. 2. García-Ramos G, Oseguera J, Nájera RG. Lipoma cardiaco. Reporte de un caso. Médica Sur 2002;9:88-90.

  3. 3. Howard RA, Aldea GS, Shapira OM, Kasznica JM, Davidoff R. Papillary fibroelastoma: increasing recognition of surgical disease. Ann Thorac Surg 1999;68:1881-1885.

  4. 4. Gowda RM, Khan IA, Nair CK, Mehta NJ, Vasavada BC, Sacchi TJ. Cardiac papaillary fibroelastoma: a comprehensive analysis of 725 cases. Am Heart J 2003;146:404-410.

  5. 5. Suminutoo S, Paterson HS. No regrowth after incomplete papillary fibroelastoma excision. Ann Thorac Surg 2005;79:3-4.

  6. 6. Oseguera GH, Valero EG, Vaca LF, Soto MP. Tumores cardiacos. En: Ruesga ZE, Jáuregui AR, Saturno CG. Cardiología. México: El Manual Moderno;2005. pp. 989-998.

  7. 7. Klarich KW, Enriquez-Sarano M, Gura GM, Edwards WD, Tajik AJ, Seward JB. Papillary fibroelastoma: echocardiographic characteristics for diagnosis and pathologic correlation. J Am Coll Cardiol 1997;30:784-790.

  8. 8. Tsukube T, Ataka K, Taniguchi T, Yokoyama M, Hanioka K. Papillary fibroelastoma of the left atrial appendage: echocardiographic findings. Ann Thorac Surg 2000;70:1416-1417.

  9. 9. Ahmed S, Nanda NC, Miller AP, Nekkanti R, Yousif AM, Pacifico AD, et al. Volume quantification of intracardiac mass lesions by transesophageal three-dimensional echocardiography. Ultrasound Med Biol 2002;28:1389-1393.

  10. 10. Grinda JM, Couetil JP, Chauvaud S, Attellis ND, Berrebi A, Fabiani JN, et al. Cardiac valve papillary fibroelastoma: surgical excision for revealed or potential embolization. J Thoracic Cardiovasc Surg 1999;117:106-110.

  11. 11. Takada A, Saito K, Ro A, Tokudome S, Murai T. Papillary fibroelastoma of the aortic valve: a sudden death case of coronary embolism with myocardial infarction. Forensic Sci Int 2000;113:209-214.

  12. 12. Okada K, Sueda T, Orihashi K, Watari M, Matsuura Y. Cardiac papillary fibroelastoma on the pulmonary valve: a rare cardiac tumor. Ann Thorac Surg 2001;71:1677-1679.

  13. 13. Crestanello JA, Orszulak TA. Giant papillary fibroelastoma of the right atrium: an unusual presentation. Ann Thorac Surg 2002;74:1252-1254.

  14. 14. Kim Hk, Kim YJ, Chang SA, Kim KB, Sohn DW, Park YB. Cardiac papillary fibroelastoma manifested as a left ventricular cystic mass. Int J Cardiol 2005;101:507-508.

  15. 15. Kurup AN, Tazelaar HD, Edwards WD, Burke AP, Virmani R, Klarich KW. Iatrogenic cardiac papillary fibroelastoma: a study of 12 cases (1990 to 2000). Hum Pathol 2002;33:1165-1169.

  16. 16. Speights VO Jr, Dobin SM, Truss LM. A cytogenetic study of cardiac papillary fibroelastoma. Cancer Genet Cytogenet 1998;103:167-169.

  17. 17. Villalpando-Mendoza E, Pérez-Pérez FM, Cortés-Flores AO, Velázquez-Ramírez GA, Fuentes-Orozco C, González-Ojeda A. Frecuencia de tumores cardiacos y su correlación histopatológica. Cir Ciruj 2006;74:183-187.

  18. 18. Koolbergen DR, Voigt P, Kolowca M, Smit VTHB, Somer ST, Dion RA. Elective surgery for fibroelastoma of the aortic valve. Ann Thorac Surg 2004;77:725.

  19. 19. Ngaage DL, Mullany CJ, Daly RC, Dearani JA, Edwards WD, Tazelaar HD, et al. Surgical treatment of cardiac papillary fibroelastoma: a single center experience with eighty-eight patients. Ann Thorac Surg 2005;80:1712-1718.

  20. 20. Nawaz MZ, Lander AR, Schussler JM, Grayburn PA, Hamman BL, Roberts WC. Tumor excision versus valve replacement for papillary fibroelastoma involving the mitral valve. Am J Cardiol 2006;97:759-764.

  21. 21. Woo YJ, Grand TJ, Weiss SJ. Robotic resection of an aortic valve papillary fibroelastoma. Ann Thorac Surg 2005;80:1100-1102.

>Journals >Cirugía y Cirujanos >Year 2007, Issue 4

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