Díaz-Pardo M, Gil-Vargas M, Aguilar-Sánchez E

Language: Spanish
References: 14
Page: 35-38
PDF size: 149.31 Kb.

ABSTRACT

Introduction: Prune Belly The term was coined by William Osler in 1901. The triad is characterized as: deficient abdominal wall musculature, urinary tract malformations (hydroureteronephrosis, megaureters) and cryptorchidism bilateral.Todos children with laxity of the abdominal wall without genitourinary malformations and girls are referred to as triad incomplete, partial or pseudoprune. For those who only manifestations is the laxity of the abdominal wall introduce the term pseudo-pseudoprune Belly.
Objective: To report the first case of the literature of a female patient with flaccid muscles of the abdominal wall in which it made plasty of the abdominal wall in the neonatal period.
Case report: Women’s 24 hrs. of life, history of prenatal ultrasound abdominal wall defect as obtained by cesarean section, A physical examination is striking only prune belly. The postnatal ultrasound reported both kidneys with reduced size and without dilatation pyelocalyceal. Intravenous urography delayed in the concentration and elimination of contrast medium in both kidneys, the size and shape of ureter and bladder and kidney gamagrama normales.El voiding cystogram showed right ureteral dilatation and bilateral grade II vesicoureteral reflux. He had surgery at 14 days of life. After two months of life merited reoperation for gastroesophageal reflux disease and alteration in the mechanics of swallowing.
Discussion: We refer to this case Belly Pseudo-pseudoprune because no genitourinary conditions specific to this pathology. The surgery in the neonatal period provides a better body image in childhood allowing to perform other surgical event simultaneously. It is striking in this patient was re abdomen without difficulty and that to date there have been no postoperative complications, besides enjoying an excellent condition.

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